Orphanet: Syndrome congenital d hamartome hypothalamique. Request PDF on ResearchGate | On Jul 1, , J. Mounach and others published Puberté précoce liée à un hamartome hypothalamique. Request PDF on ResearchGate | On May 1, , N. Ech-Cherif El Kettani and others published Hamartome hypothalamique révélant des crises gélastiques.

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Drop attacks and other secondary generalized epilepsy symptoms usually develop as the patient ages. Access to the text HTML. Careful planning and a stepwise approach with the advanced surgical technique will make it possible 24 Their classification was based on either pedunculated or sessile sagittal orientation and the treatments included open surgical removal or medicinal intervention.

There should be minimal working space within the third ventricle for forceps and coagulator, as well as definite interface either on the neuronavigational image or direct visualization.

Surgical approaches with open craniotomy or endoscopy, stereotactic approaches with radiosurgery hypothalakique gamma knife surgery or radiofrequency thermos-coagulation, and laser ablation have been introduced.

Discrete appearance of HHs to show the interface between HHs and the hypothalamus. Hypothalamic hamartomas associated with epilepsy: Kyu Won ShimM.

Translation of “hypothalamus hamartome” in English

Retrospective analysis of surgical treatment outcomes for gelastic seizures: Transendoscopic intraoperative recording of gelastic seizures from a hypothalamic hamartoma.

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As the authors describe 31even giant HHs larger than 25 mm can be efficiently disconnected under guidance of a depth electrode and frameless neuronavigation system. Platinum microwire intraoperative recording of single neuron activity captured 10—20 spikes per second in over HH neurons from 14 patients. However, it did reveal a very important feature that sessile-type HHs usually cause GSs 1 Therefore, concomitant scalp EEG and depth electrode recording inside HHs may be very useful in disconnecting this lesion from intractable epilepsy.


Transient short-term memory loss, weight gain, thalamic infarction with memory loss, and hemiparesis have been reported as early complications. Hypothalamic hamartoma HH is a benign indolent lesion despite the presentation of refractory epilepsy. Hypothalamic hamartoma and seizures: Recently stereotactic laser ablation has been introduced and good seizure control has been achieved.

Endoscopic Treatment of Hypothalamic Hamartomas

Journal page Archives Contents list. However, most intraventricular HHs are excellent candidates for endoscopic resection or disconnection 823 Le syndrome hamartome hypothalamique: However, surgical resection for total removal of HHs have led to good seizure outcomes and behavioral improvement 10 Electric recording through depth electrode and transendoscopic intraoperative hypohtalamique are also hypothalamisue of recording the epileptic activities of HHs 21 Because most of the patients have small ventricles, usually a neuronavigation system is set before beginning the main surgical procedure.

Recent electroencephalography-functional magnetic resonance image EEG-fMRI studies revealed that the ipsilateral hypothalamus, brainstem tegmentum, and contralateral cerebellum are activated. Three of four patients with postoperative disconnection-like syndrome mental dullness, verbal anomia, unilateral tactile anomia, and lack of somesthetic transfer were observed by Choi et al.

Chabrol abF. Modern imaging techniques and subsequent state of the art technology in surgical image guidance systems are critical to performing this delicate job An optimal surgical approach should be selected based on the individual status of the lesion and the patient Fig.

National Center for Biotechnology InformationU. Access to the text HTML.


Endoscopic Treatment of Hypothalamic Hamartomas

Report of four cases. A monopolar-coagulating electrode or an Nd-Yag laser system, a fiberoptic hypothalamiqke guide, an Xe light source, and an endovision system are other supporting instruments. Endoscopic resection of hypothalamic hamartomas for refractory symptomatic epilepsy. In bilateral attachment and giant HH cases, preoperative electrophysiological evaluation mostly revealed unilateral propagation of epileptiform discharge 31 Ictogenesis and symptomatogenesis of gelastic seizures hypothalamiwue hypothalamic hamartomas: Role of the hypothalamic hamartoma in the genesis of gelastic fits a video-stereo-EEG study Electroencephalogr Clin Neurophysiol.

Autonomic and hormonal ictal changes in gelastic seizures from hypothalamic hamartomas. Endoscopic approach to hypothalamic hamartoma HHs. An immediate seizure-free condition was the single most reliable factor for long-term seizure outcome.

hypothalamus hamartome – Translation into English – examples French | Reverso Context

The histopathology of hypothalamic hamartomas: The mass should not be under the optic tract. Other types of seizure, cognitive deterioration, and behavioral problems follow and frequently develop late in the first decade of life 4 But even though HHs attach to the bilateral hypothalamus, unilateral disconnection is usually enough. Here we discuss hypotgalamique evaluation, patient selection, surgical procedures, and complications.

Zerhouni aA. The depth electrode will guide the disconnection surgery as well as confirm the successful disconnection 28 When the thin pial membrane or arachnoid membrane is reached, dissection is complete. hanartome

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Last modified: January 2, 2020